2-Hydroxyisovalerylcarnitine

(3R)-3-[(2R)-2-hydroxy-3-methylbutanoyl]oxy-4-(trimethylazaniumyl)butanoate

FANTUGMIEAASNP-MWLCHTKSSA-N CHEBI:192727 0 Reactome links 1 studies

1 Observed studies

1 Observed diff profiles

0 Reactome pathways

Metabolite details

Identifier: FANTUGMIEAASNP-MWLCHTKSSA-N
InChI Key: FANTUGMIEAASNP-MWLCHTKSSA-N
IUPAC name: (3R)-3-[(2R)-2-hydroxy-3-methylbutanoyl]oxy-4-(trimethylazaniumyl)butanoate
Preferred name: 2-Hydroxyisovalerylcarnitine
INN name: —
Synonym: —
ChEBI: CHEBI:192727

Reactome pathways

No Reactome pathways listed for this metabolite.

Observed in studies

Distinct succinate modifying products are clinically diagnostic and prognostic biomarkers for fumarate hydratase deficient renal cell carcinoma

Observed in differential profiles

Normal_control_no_tumor_vs_FH_deficient_RCC